The Spectrum of Mitochondrial Ultrastructural Defects in Mitochondrial Myopathy
نویسندگان
چکیده
منابع مشابه
The Spectrum of Mitochondrial Ultrastructural Defects in Mitochondrial Myopathy
Mitochondrial functions are intrinsically linked to their morphology and membrane ultrastructure. Characterizing abnormal mitochondrial structural features may thus provide insight into the underlying pathogenesis of inherited and acquired mitochondrial diseases. Following a systematic literature review on ultrastructural defects in mitochondrial myopathy, we investigated skeletal muscle biopsi...
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ژورنال
عنوان ژورنال: Scientific Reports
سال: 2016
ISSN: 2045-2322
DOI: 10.1038/srep30610